Electroencephalographic and epidemiological characterization of patients with West Syndrome

Authors

DOI:

https://doi.org/10.36958/sep.v8i2.373

Keywords:

West syndrome, hypsarrhythmia, epileptic activity

Abstract

OBJECTIVE: to describe the electroencephalographic findings in children with West syndrome treated in the Pediatric Neurology Unit of San Juan de Dios General Hospital. METHODS: descriptive, retrospective, observational. RESULTS: the basic electroencephalographic activity found in the patients studied according to sex showed a predominance of abnormal results in males with 52.58% and females with 44.44%. It is noteworthy that 2.78% of the males had a normal result, which was not observed in any female participant. CONCLUSIONS: abnormal EEG activity, in order of frequency, was typical hypsarrhythmia (36.11%), focal epileptic activity (16.67%), generalized epileptic activity and hypsarrhythmia with episodes of voltage attenuation (11.11%). The other types of abnormalities did not have clear predominance.

Downloads

Download data is not yet available.

Author Biography

Ana Cristina Arévalo Díaz, Universidad Galileo

Completed curriculum for the Master's Degree in Medical Sciences with a specialization in Clinical Neurophysiology from the University of San Carlos of Guatemala, Master's Degree in Geriatrics and Gerontology from the Galileo University, and Specialization Studies in Research from the University of San Carlos of Guatemala.

References

Aicardi, J. (1992). Postnatally acquired infectious diseases. In: Aicardi J, ed. Diseases of the Nervous System in Childhood, 2ª edición. Londres: McKeith Press 1992:590-6. https://www.ilae.org/files/ilaeBook/samplePages/Aicardi-4th-ed-Diseases-of-Nervous-system-in-childhood-supp.pdf

Álvarez Valdez, VH. (2018). Caracterización Epidemiológica, Clínica y Factores de Riesgo en Pacientes con Diagnóstico De Epilepsia, (Tesis de Pregrado, previo a optar al título de Médico y Cirujano en grado de Licenciatura), Universidad de San Carlos de Guatemala. https://biblioteca.medicina.usac.edu.gt/tesis/pre/2018/005.pdf

Appendino, J. A. & Appendino, J. I. (2019). Encefalopatías epilépticas determinadas genéticamente. Clinical Neuroscience Departament of Pediatrics, Alberta Children´s Hospital, Cumming School of Medicine, University of Calgary, Alberta Canadá, Servicio de Neurología Pediátrica Departamento de Pediatría, Hospital Italiano de Buenos Aires, Argentina. Artículo especial Medicina, Buenos Aires, 2019. Volumen 79, (Supl III) 42-47. http://trovare.hospitalitaliano.org.ar/greenstone/collect/revistas/index/assoc/D1080.dir/articulo-publicado-appedino-2019.pdf

Arcas Martínez, J. (2011). Presente y futuro de los síndromes epilépticos pediátricos. Servicio de Neuropediatría del Hospital Infantil “La Paz”, Madrid. Editorial Centro de estudios Ramón Areces, S.A. Fundación Ramón Areces S.A. pp. 39-52. http://www.sindromedewest.org/PDF/LIBROS/Libro_1.pdf

Arce Portillo, E., Rufo Campos, M., Muñoz Cabello, B., Blanco Martínez, B., Madruga Garrido, M., Ruiz Del Portal, L. y Candau Fernández Mensaque, R. (16 Ene 2011). Síndrome de West: etiología, opciones terapéuticas, evolución clínica y factores pronósticos / Rev. neurol. (Ed. impr.); 52(2): 81-89. https://pesquisa.bvsalud.org/portal/resource/pt/ibc-86966

Arroyo Cartagena, M.F., Jaramillo Oyervide, J.A. (2018, noviembre). Síndrome de West. Hospital. Revista de la Facultad de Ciencias Médicas. 36(2), 70-74. https://publicaciones.ucuenca.edu.ec/ojs/index.php/medicina/article/view/2500

Calderón Romero, M., Arce Portillo, E., López Lobato, M., Muñoz Cabello, B., Blanco Martínez B., Madruga Garrido, M. y Alonso Luego, O. (2018). Síndrome de West criptogénico: perfil clínico, respuesta al tratamiento y factores pronósticos. Anales de Pediatría, 89(3), 176-182. www.analesdepediatria.org

Calvo, A., Terrazas, R., Mercado, C., Caballero, R., Gallo, A., Caraballo, R. y Pérsico A. (Abr 2019). Encefalopatías Epilépticas: revisión actualizada. Revista Chilena de Epilepsia. 19(1), 25-57. https://www.ilae.org/files/dmfile/Revista-Chilena-de-Epilepsia-2019-04.pdf

Caraballo, R., Cersósimo, R., Arroyo, H. y Fejerman, N. (1998) Síndrome de West sintomático: asociaciones etiológicas particulares con respuesta inesperada al tratamiento. Rev Neurol, 26 (151), 372-375. https://files.neurologia.com/journal/RN/26/151/10.33588/rn.26151.98953/pdf/74c35ee0796dabb61bc1000cd60ab0b7.pdf

Demarest, S. T., Shellhaas, R. A., Gaillard, W. D., Keator, C., Nickels, K. C., Hussain, S. A., et al. The impact of hypsarrhythmia on infantile spasms treatment response: Observational cohort study from the National infantile spasms consortium. Epilepsia 58(12), 2098-2103. https://doi.org/10.1111/epi.13937

Hrachovy, R. A., Frost, J. D. & Kellaway, P. (1984). Hypsarrhythmia: Variations on the Theme, Epilepsia, 25(3), 317-325. https://doi.org/10.1111/j.1528-1157.1984.tb04195.x

Kajimoto, M., Ichiyama, T., Akashi, A., Suenaga, N., Matsufuji, H., & Furukawa, S. (2007). West syndrome associated with mosaic Down syndrome. Brain & development, 29(7), 447–449. https://doi.org/10.1016/j.braindev.2006.12.006

López Poveda, L. M. (2016, mayo). Encefalopatía epiléptica, Síndrome de West. (Tesis de Pregrado, previo a optar al título de Médico y Cirujano en grado de Licenciatura), Universidad Técnica de Ambato, Facultad de Ciencias de la Salud, Ambaro, Ecuador. http://repositorio.uta.edu.ec/bitstream/123456789/23101/2/L%C3%B3pez%20Poveda%2C%20Lucia%20Maribel.pdf

Nelson, G. (2015) Management of infantile spasms. Translational Pediatrics, 4(4), 260-270. http://dx.doi.org/10.3978/j.issn.2224-4336.2015.09.01

Pavone, P., Polizzi, A., Marino, S. D., Corsello, G., Falsaperla, R., Marino, S., & Ruggieri, M. (2020). West syndrome: a comprehensive review. Neurological sciences: official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology, 41(12), 3547–3562. https://doi: 10.1007/s10072-020-04600-5

Pramote, L. (2013). Epileptic encephalopathy. Laoprasert P(Ed.), Atlas of Pediatric EEG. McGraw-Hill Education. https://neurology.mhmedical.com/content.aspx?bookid=1042&sectionid=59078729

Sanz Arrazola, H. & Berazain, C. A. (2014). Síndrome de West: etiología, fisiopatología, aspectos clínicos, diagnóstico, tratamiento y pronóstico. Neurología. Revista Médico-Científica “Luz y Vida”, 5(1), 30-35. http://www.redalyc.org/articulo.oa?id=325038650007

Published

10-12-2025

How to Cite

Arévalo Díaz, A. C. (2025). Electroencephalographic and epidemiological characterization of patients with West Syndrome. Revista Cientí­fica Del Sistema De Estudios De Postgrado De La Universidad De San Carlos De Guatemala, 8(2), 33–45. https://doi.org/10.36958/sep.v8i2.373

Issue

Section

Scientific articles

Categories

Similar Articles

1 2 3 > >> 

You may also start an advanced similarity search for this article.